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2.4.1.B80: alpha-dystroglycan glucuronosyltransferase

This is an abbreviated version!
For detailed information about alpha-dystroglycan glucuronosyltransferase, go to the full flat file.

Word Map on EC 2.4.1.B80

Reaction

UDP-alpha-D-glucuronate
+
alpha-D-xylosyl-(1->3)-[3)-beta-D-glucuronosyl-(1->3)-alpha-D-xylosyl-(1->]n-[O-mannosyl-chain of alpha-dystroglycan]
=
UDP
+
beta-D-glucuronosyl-(1->3)-alpha-D-xylosyl-(1->3)-[3)-beta-D-glucuronosyl-(1->3)-alpha-D-xylosyl-(1->]n-[O-mannosyl-chain of alpha-dystroglycan]

Synonyms

LARGE1, like-acetylglucosaminyltransferase

ECTree

     2 Transferases
         2.4 Glycosyltransferases
             2.4.1 Hexosyltransferases
                2.4.1.B80 alpha-dystroglycan glucuronosyltransferase